Juvenile musculoaponeurotic fibromatoses are benign tumors which arise from musculoaponeurotic stromal cells. They rarely occur in lower extremity and more rarely in children. They are locally invasive tumors with a high incidence of recurrence after surgery. Hence, wide local excision is the treatment of choice for such tumors. However, complex reconstruction is often required to cover the resulting soft tissue defect. This report presents a 12-year-old boy with a juvenile musculoaponeurotic fibromatosis in the anteromedial aspect of the upper third of a left leg. Following wide local excision, two local flaps, medial gastrocnemius and a distally based peroneal artery perforator flap, were used to reconstruct the soft tissue defect. Reconstruction has provided an acceptable functional and cosmetic result.
Stout AP (1954) Juvenile fibromatoses. Cancer 7:953-978
Mackenzie DH (1972) The fibromatoses: a clinicopathological concept. Br Med J 4:277-281
Tolhurst DE, Haeseker B, Zeeman RJ (1983) The development of fasciocutaneus flap and its application. Plast Reconstr Surg 71:597
Mathes S, Nahai F (1982) Clinical application of muscles and musculocutaneous flaps. Mosby, St. Louis
Chaudhuri B, Das Gupta TK (1998) Pathology of soft tissue sarcomas. In: Das Gupta TK, Chaudhuri PK (eds) Tumors of the soft tissues. Appleton and Lange, Stanford, pp 63-200
Reitamo JJ, Scheinin TM, Havry P (1986) The desmoid syndrome. New aspects in the cause, pathogenesis and treatment of the desmoid tumor. Am J Surg 151:230-237
Dahn J, Johnson N, Lundh G (1963) Desmoid tumours. A series of 33 cases. Acta Chir Scand 126:305-314
McAdam WAF, Goligher JC (1970) The occurrence of desmoids in patients with familial polyposis coli. Br J Surg 57:618-631
Hansmann A, Adolph C, Vogel T, Unger A, Moeslein G (2004) High-dose tamoxifen and sulindac as first-line treatment for desmoids tumors. Cancer 100:612-620
Lee J, Glazer H (1990) Controversy in the MR imaging of fibrosis. Radiology 177:21-22
Abbas AE, Deschamps C, Cassivi SD, Nichols FC III, Allen MS, Schleck CD, Pairolero PC (2004) Chest-wall desmoid tumors: results of surgical intervention. Ann Thorac Surg 78:1219-1223
Lewis JJ, Boland PJ, Leung DH et al (1999) The enigma of desmoids tumors. Ann Surg 229:866-887
Nuyttens JJ, Rust PF, Thomas CR, Turrisi AT III (2000) Surgery versus radiation therapy for patients with aggressive fibromatosis or desmoids tumors. A comparative review of 22 articles. Cancer 88:1517-1523
