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VOLUME 11 , ISSUE 3 ( November, 2016 ) > List of Articles

Original Article

Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience

John Ham, Mark Flipsen, Marianne Koolen, Arnard van der Zwan, Konrad Mader

Keywords : Multiple hereditary exostoses (MHE), Multiple osteochondromas (MO), Masada classification, Forearm reconstruction, Corrective osteotomy, External fixation, Review

Citation Information : Ham J, Flipsen M, Koolen M, van der Zwan A, Mader K. Multiple osteochondromas (MO) in the forearm: a 12-year single-centre experience. 2016; 11 (3):169-175.

DOI: 10.1007/s11751-016-0267-1

License: CC BY-NC-SA 4.0

Published Online: 30-11-2016

Copyright Statement:  Copyright © 2016; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Multiple osteochondromas (MO) are a rare autosomal dominant disorder characterized by the presence of osteochondromas located on the long bones and axial skeleton. Patients present with growth disturbances and angular deformities of the long bones as well as limited motion of affected joints. Forearm involvement is found in a considerable number of patients and may vary from the presence of a simple osteochondroma to severe forearm deformities and radial head dislocation. Patients encounter a variety of problems and symptoms e.g., pain, functional impairment, loss of strength and cosmetic concerns. Several surgical procedures are offered from excision of symptomatic osteochondromas to challenging reconstructions of forearm deformities. We describe visualizing, planning and treating these forearm deformities in MO and, in particular, a detailed account of the surgical correction of Masada type I and Masada type II MO forearm deformities.


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